Abstract: In recent years， there are more and more studies and reports about autoimmune diseases （ADs） associated with non-Hodgkin lymphoma （NHL）. Now it has been found that many ADs will increase the risk of NHL，but different types of ADs contribute different risk of NHL， with a certain tendency in the pathological type of NHL. The biological mechanism of this phenomenon is worth to explore further. In this article，we will review the current study of ADs which associated with increased risk of NHL and the clinical features， biological mechanisms and treatment of ADs associated with NHL.